Hi, management of IPAH includes: medical management,
A single- or double-lung transplant is indicated for patients who do not respond to medical therapy.
Atrial septostomy is a palliative procedure that may afford some benefit to patients whose condition is deteriorating.
IPAH has no cure. Untreated IPAH leads to right-sided heart failure and death.
For untreated IPAH, the estimated 3-year survival rate is approximately 41%.
Answered2015-09-11 06:33:35
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